Fluorogenic soluble enzyme substrate for α-L-iduronidase. α-L-iduronidase is deficient in the genetic disorder Mucopolysaccharidosis type I, also called Hurler syndrome. Diagnosis of Hurler syndrome involves enzymatic assay of α-L-iduronidase activity using the fluorogenic enzyme substrate 4-Methylumbelliferyl-α-L-iduronide.
