89-7795-80 Recombinant Human b-Galactosidase/GLB1 Protein (His Tag) 10ug PKSH033267
[Elabscience]
特徴
- 背景：b Galactosidase is a lysosomal b Galactosidase that hydrolyzes the terminal b Galactose from Ganglioside and Keratan sulfate. In lysosome, the mature b Galactosidase protein associates with Cathepsin A and Neuraminidase 1 to form the lysosomal multienzyme complex . An alternative splicing at the RNA level of b Galactosidase results a catalytically inactive b Galactosidase that plays an important role in vascular development. Defects of b-galactosidase (GLB1) are the cause of diseases like GM1-gangliosidosis which is a lysosomal storage disease and Morquio Syndrome B that cause patients to have abnormal elastic fibers. More than 100 mutations have been identified for b Galactosidase, which result in different residual activities of the mutant enzymes and a spectrum of symptoms in the two related diseases.
仕様
- サイズ：10ug
- 種由来：Human
- 発現宿主：Human Cells
- 純度：> 95 % as determined by reducing SDS-PAGE.
- エンドトキシン濃度：< 1.0 EU per ug as determined by the LAL method.
- アクセッションＮｏ．：P16278
- タグ種類：C-6His
- アミノ酸配列：Leu24-Val677
- 遺伝子構造：Recombinant Human beta-Galactosidase is produced by our Mammalian expression system and the target gene encoding Leu24-Val677 is expressed with a 6His tag at the C-terminus.
- 別名（遺伝子名）：Beta-Galactosidase; Acid Beta-Galactosidase; Lactase; Elastin Receptor 1; GLB1; ELNR1
- 分子量：74.6 kDa
- 組成：Supplied as a 0.2 μm filtered solution of 20mM TrisHCl, 150mM NaCl, pH 8.0.
- 保存条件：Store at < -20°C, stable for 6 months. Please minimize freeze-thaw cycles.
- メーカーマニュアルリンク：https://www.elabscience.com/viewpdf-106928-Elabscience-PKSH033267.pdf
- この商品は法規制を確認しておりません。（法規制によって販売できない場合もございます）
- 【試薬に関するお問合せ】
- アズワン株式会社 試薬・プロセス材料グループ
- TEL：06-6447-8641
- FAX：06-6447-8642
- E-mail：[email protected]
商品のバリエーション （サイズ違い・スペック違い・オプション品など）
| 商品イメージ | アズワン品番 商品名 |
|---|---|
|
89-7795-80
Recombinant Human b-Galactosidase/GLB1 Protein (His Tag) 10ug
|
|
|
89-7795-81
Recombinant Human b-Galactosidase/GLB1 Protein (His Tag) 50ug
|
よくあるご質問（FAQ）
掲載カタログ情報
| 掲載カタログ名 | 掲載ページ |
|---|