Background：The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB （encoding the beta subunit） lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.
仕様
Synonyms：mitochondrial,Pcca,pccA COMPLEMENTATION GROUP,PCCA,PCCase subunit alpha,Propanoyl CoA：carbon dioxide ligase subunit alpha ,Propanoyl-CoA：carbon dioxide ligase subunit alpha,Propionyl CoA carboxylase alpha chain,Propionyl CoA carboxylase alpha chain mitochondrial,Propionyl CoA carboxylase alpha polypeptide,Propionyl coenzyme A carboxylase alpha polypeptide ,Propionyl-CoA carboxylase alpha chain
Host：Rabbit
Reactivity：Human,Mouse,Rat
Applications：WB
Concentration：1mg/ml
Immunogen：Recombinant protein of human PCCA
Purification Method：Affinity purification
Clonality：Polyclonal
Conjugation：Unconjugated
Buffer：Buffer： PBS with 0.02％ sodium azide, 50％ glycerol, pH7.3.
