Background:This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
仕様
Synonyms:3 methylcrotonyl CoA carboxylase 2 ,3 methylcrotonyl CoA carboxylase non biotin containing subunit,3 methylcrotonyl CoA:carbon dioxide ligase subunit beta,3-methylcrotonyl-CoA carboxylase 2,3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit,3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta,Biotin carboxylase,MCCase subunit beta,MCCB,MCCB,MCCC 2,Mccc2,Methylcrotonoyl CoA carboxylase 2 (beta),Methylcrotonoyl CoA carboxylase beta chain mitochondrial,Methylcrotonoyl Coenzyme A carboxylase 2 (beta),Methylcrotonoyl-CoA carboxylase beta chain,mitochondrial,Non biotin containing subunit of 3 methylcrotonyl CoA carboxylase
Host:Rabbit
Reactivity:Human,Mouse,Rat
Applications:WB,IHC
Concentration:1mg/ml
Immunogen:Recombinant protein of human MCCC2
Purification Method:Affinity purification
Clonality:Polyclonal
Conjugation:Unconjugated
Buffer:Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.