Background:Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
仕様
Synonyms:ACAD2,FLJ12715,FLJ34849,Isovaleryl CoA dehydrogenase,Isovaleryl CoA dehydrogenase,mitochondrial,Isovaleryl Coenzyme A dehydrogenase,Isovaleryl-CoA dehydrogenase,IVD,IVD,mitochondrial
Host:Rabbit
Reactivity:Human,Mouse
Applications:WB
Concentration:1mg/ml
Immunogen:Recombinant protein of human IVD
Purification Method:Affinity purification
Clonality:Polyclonal
Conjugation:Unconjugated
Buffer:Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.