Background：This gene encodes a glycoprotein which associates with lysosomal enzymes beta-galactosidase and neuraminidase to form a complex of higHuman, Mouseolecular weight multimers. The formation of this complex provides a protective role for stability and activity. Deficiencies in this gene are linked to multiple forms of galactosialidosis. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
仕様
Synonyms：beta galactosidase 2,BETA GALACTOSIDASE PROTECTIVE PROTEIN,beta-galactosidase 2,beta-galactosidase protective protein,betagalactosidase 2,Carboxypeptidase C,Carboxypeptidase L,carboxypeptidase Y-like kininase,Cathepsin A,Ctsa,deamidase,EC 3.4.16.5,Glactosialidosis,GLB2,Goldberg Syndrome,GSL,lysosomal carboxypeptidase A,Lysosomal protective protein 20 kDa chain,Lysosomal protective protein,Lysosomal protective protein deficiency,NEURAMINIDASE BETA GALACTOSIDASE EXPRESSION,NGBE,Neuraminidase deficiency with beta-galactosidase deficiency,NGBE,OTTHUMP00000031778,OTTHUMP00000031781,PPCA,PPCA deficiency,PPGB,PPGB,Protective protein cathepsin A,Protective protein for beta galactosidase,Protective protein for beta-galactosidase,Protective protein/cathepsin A deficiency,urinary kininase
Host：Rabbit
Reactivity：Human,Mouse
Applications：WB,ELISA
Concentration：0.3mg/mL
Immunogen：Recombinant protein of human CTSA
Purification Method：Affinity purification
Clonality：Polyclonal
Conjugation：Unconjugated
Buffer：PBS with 0.05％ sodium azide, 50％ glycerol, PH7.3
Dilution：WB 1：200-1：1000
Swissprot：P10619
Isotype：IgG
Research Areas：Cancer, Metabolism, Signal transduction
