85-5957-93　β-Hydroxyisovaleric Acid-d8 10mg　469713

特徴

• β-Hydroxyisovaleric Acid-d8 is the isotope labeled analog of β-Hydroxyisovaleric Acid; a metabolite of the essential amino acid Leucine. It is synthesized in the human body and studies suggest that β-Hydroxyisovaleric Acid may have an effect on increasing muscle weight and strength. The presence of elevated β-Hydroxyisovaleric Acid is a sensitive marker of biotin deficiency and may indicate the presence of a genetic disorder such as biotinidase deficiency or holocarboxylase synthetase deficiency.
• Synonyms:3-Hydroxy-3-methylbutanoic Acid-d8; 3-Hydroxy-3-methylbutyric Acid-d8; 3-Hydroxyisovaleric Acid-d8; β-Hydroxy-β-methylbutyric Acid-d8
• Molecular Formula:C₅H₂D₈O₃
• Molecular Weight:126.18
• Purity:≥97% (Isotopic)
• Appearance:Colorless to yellow oil
• Solubility:DMSO (Sparingly), Methanol (Slightly)
• Method for Determining Identity:H NMR and C NMR Spectrometric Analysis and Mass Spectrometric Analysis
• TLC Conditions:SiO2; Dichloromethane: Methanol: Acetic Acid=8:1:0.1; Visualized with AMCS; Single Spot, Rf=0.65
• Normalized Intensity:d0=0.00%, d1=0.00%, d2=0.01%, d3=0.03%, d4=0.00%, d5=0.07%, d6=0.31%, d7=4.48%, d8=95.10%
• Storage and Stability:May be stored at RT for short-term only. Long-term storage is recommended at 4ºC for 6 months after time of receipt.