84-5465-55 ［取扱停止］FAM111B 30ul 536222
特徴
- FAM111B encodes a protein with a trypsin-like cysteine/serine peptidase domain in the C-terminal.
- Mutations in this gene are associated with an autosomal dominant form of hereditary fibrosing poikiloderma (HFP).
- Affected individuals display mottled pigmentation, telangiectasia, epidermal atrophy, tendon contractures, and progressive pulmonary fibrosis.
- Alternative splicing results in multiple transcript variants encoding distinct isoforms.
- A paralog of this gene which also has a trypsin-like peptidase domain, FAM111A, is located only 16kb from this gene on human chromosome 11q12.
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- Applications:Suitable for use in Immunohistochemistry and ELISA.
- Other applications not tested.
- Recommended Dilution:Immunohistochemistry (paraffin): 1:100-1:300ELISA: 1:5000Optimal dilutions to be determined by the researcher.
- Storage and Stability:May be stored at 4°C for short-term only.
- Aliquot to avoid repeated freezing and thawing.
- Store at -20°C.
- Aliquots are stable for 12 months after receipt.
- For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
仕様
- Size：30ul
- Host：rabbit
- Source Antibody：human
- Grade：Affinity Purified
- Purity：Purified by immunoaffinity chromatography.
- Form：Supplied as a liquid in PBS, 0.5% BSA, 0.02% sodium azide, 50% glycerol.
- Specificity：Recognizes endogenous levels of human FAM111B.
- Isotype：IgG
- Calc Applications Abbrev：E IHC
- Calc Crossreactivity：Hu
- Immunogen：Synthetic peptide corresponding to aa250-330 of human FAM111B.
- Swiss Prot Number：Q6SJ93
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