84-2377-85　［取扱停止］PCCB (PCCase Subunit beta, pccB, PCCB_HUMAN, pccBC Complementation group, Propanoyl CoA:carbon dioxide Ligase Subunit beta, Propanoyl-CoA:carbon dioxide Ligase Subunit beta, Propionyl CoA Carboxylase beta Chain, Mitochondrial, propionyl Coenzyme A Carboxylase, beta Polypeptide, Propionyl-CoA Carboxylase , beta Subunit, Propionyl-CoA Carboxylase beta Chain, Mitochondrial, R74805,) 100ul　224903

特徴

• The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA.
• PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits.
• This gene encodes the beta subunit of PCC.
• Defects in this gene are a cause of propionic acidemia type II (PA-2).
• Multiple transcript variants encoding different isoforms have been found for this gene.
• Applications:Suitable for use in Western Blot, Immunohistochemistry.
• Other applications not tested.
• Recommended Dilution:Western Blot: 1:500-1:2000Immunohistochemistry: 1:50-1:200Optimal dilutions to be determined by the researcher.
• Storage and Stability:May be stored at 4°C for short-term only.
• Aliquot to avoid repeated freezing and thawing.
• Store at -20°C.
• Aliquots are stable for 12 months after receipt.
• For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.